Abstract

Epidermolysis bullosa (EB) is a rare (1/17000-1/300000) genetic disease which is characterized by an abnormal collagen and extreme fragility of skin and mucous membranes. We report successful management of a 24-year-old-woman with epidermolysis bullosa presented to operation room for local resection of mass on tuberositas tibia under general anesthesia with laryngeal mask airway. Anesthesia management of EB cases requires features at all stages of anesthesia management. A multidisciplinary approach and careful planning are essential for safely management of surgery.

Key words: Epidermolysis bullosa; general anesthesia; laryngeal mask airway