Abstract

Stiff skin syndrome (SSS) is a rare cutaneous disease starting in infancy or early childhood characterized by stony hard skin specificaly around thighs and buttocs, by joint mobility limitation and by mild hypertrichosis. It does not present visceral or muscle involvement. By presenting a patient presumed to be SSS due to start of the disease and clinical features we intented to emphasize its differances from scleroderma.

Key words: Stiff skin syndrome, scleroderma