Objective: Intracranial extraskeletal myxoid chondrosarcoma is a rare tumor; up to date, only ten cases have been reported.
Case report: We present a case report of a 65-year-old female admitted for right side hemiplegia of gradual onset and progressive course over three weeks. Magnetic resonance imaging (MRI) revealed left intra-axial parieto-occipital space occupying lesion, hypodense with ring enhancement surrounded by diffuse edema. The patient underwent subtotal resection of the mass using sonar guided craniotomy. The histopathological and immunohistochemical evaluation confirmed a diagnosis of extraskeletal myxoid chondrosarcoma. One month after initial discharge, the patient underwent radiotherapy. A follow-up examination 6 months after surgery revealed that the patient was deteriorated and died.
Conclusion: intracranial extraskeletal myxoid chondrosarcoma is a rare malignant cartilaginous tumor. Pathological diagnosis is the gold standard and radical excision is the standard treatment
Intracranial tumor, Chondrosarcoma, Central nervous system