Home|Journals|Articles by Year|Audio Abstracts
 

Original Article



Surgical treatment results of hand deformities in patients with Apert syndrome

Ufuk Nalbantoglu, Tekin Kerem Ulku, Arel Gereli, Metin Turkmen.




Abstract

Objectives: Hand deformities in Apert sydrome are complex pathologies and usually consist of complex syndactyly with distal bony fusion in the 2., 3. and 4th fingers, simple syndactyly in the 5th finger, and short thumb, radial clinodactily and synphalangism. Other accompanying deformities and the presence of craniosynosthosis make the treatment plan even more complex. Because it is such a rare disorder, no standard treatment protocol has yet been developed.
Methods: In this study, our aim was to evaluate the early results of our standard treatment protocol for Apert’s hands. We evaluated 7 patients with Apert’s hands who were treated bilaterally between the years of 2008 and 2013. We performed a two-stage surgical protocol, the first of which was the bilateral opening of the border fingers and the second stage was the opening of the middle fingers and web space deepening, osteotomy and collateral release of the thumb. Patients were evaluated according to grasping and pinching ability, graft-flap necrosis and cosmetic satisfaction.
Results: The mean age at the first operation was 2.7 years and the mean number of operations was 3 per patient. No patient developed graft-flap necrosis and no patients required amputations. All patients were able to perform grasping and pinching functions and families were satisfied with the cosmetic results.
Conclusion: Using a two-stage surgical protocol, achieving satisfactory results with a minimal number of operations is possible in patients with Apert Syndrome.

Key words: Apert syndrome, hand deformity, syndactily






Full-text options


Share this Article


Online Article Submission
• ejmanager.com




ejPort - eJManager.com
Refer & Earn
JournalList
About BiblioMed
License Information
Terms & Conditions
Privacy Policy
Contact Us

The articles in Bibliomed are open access articles licensed under Creative Commons Attribution 4.0 International License (CC BY), which permits use, sharing, adaptation, distribution and reproduction in any medium or format, as long as you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons licence, and indicate if changes were made. To view a copy of this licence, visit http://creativecommons.org/licenses/by/4.0/.