The congenital constriction band syndrome of lower extremity is a very uncommon and well-described disease which includes several congenital deformities. The true incidence in general population is unknown. The type of malformation depends on the time of gestational period. Although congenital constriction band syndrome is a well-known congenital condition, the development mechanism of this anomaly has not been clarified fully. There are many intrinsic and extrinsic theories regarding the etiology of this rare syndrome. Generally accepted mechanism is the process that consists of the early amniotic rupture leading to formation of mesodermal fibrous strands which constrict and amputate distal portions of limbs. It is characterized by syndactyly, hypoplasia, brachydactyly, symphalangism, symbrachydactyly, club foot, cleft lip, cleft palate, and cranial defects. The lesion can involve skin only or goes to deeper structure up to bone, which can lead to gangrene of foot or autoamputation. The treatment should be tailored to the individual patient. The aim of surgical treatment requires release of deep as well as superficial structures. We are presenting a patient with constriction band syndrome which has been treated because of late onset beginning of entrapment neuropathy at his left leg. To our knowledge, no such cases have been previously reported in the literature.
Key words: Amniotic band, congenital constriction band syndrome, deformity, entrapment, neuropathy
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