Background: Granular cell tumors are rare soft tissue neoplasms probably derived from Schwann cells. They account for 0.5% of all soft tissue tumors. They might occur at any site and most commonly involve tongue, breast, upper respiratory tract, and upper extremities soft tissue. Usually, granular cell tumors are benign, and only less than 2% are malignant, but these are aggressive and associated with a poor prognosis.
Case Presentation: The case presented in the current study showed atrophied fibrotic plaque resembling localized scleroderma and panniculitis. A 16-year-old female with a 6-year history of painless atrophied fibrotic plaque over the left forearm was presented. The first clinical impression was to rule out morphea; however, subsequent histopathologic examination confirmed the diagnosis of benign cutaneous granular cell tumor with S100 positivity.
Conclusion: A granular cell tumor is rare and most often presented as a benign tumor. It occurs at different body sites. Histopathology is required to confirm the diagnosis. Wide local excision is recommended as the first line of treatment for benign cases.
Key words: Atypical presentation, granular cell tumor, fine needle aspiration cytology, case report
|
